http://www.cnr.it/ontology/cnr/individuo/prodotto/ID7568
Management of children with Thrombocytopenia-absent radius syndrome: An institutional experience. (Articolo in rivista)
- Type
- Label
- Management of children with Thrombocytopenia-absent radius syndrome: An institutional experience. (Articolo in rivista) (literal)
- Anno
- 2012-01-01T00:00:00+01:00 (literal)
- Http://www.cnr.it/ontology/cnr/pubblicazioni.owl#doi
- 10.1111/j.1440-1754.2011.02069.x (literal)
- Alternative label
Coccia, P.; Ruggiero, A.; Mastrangelo, S.; Attinà, G.; Scalzone, M.; Pittiruti, M.; Zampino, G.; Maurizi, P.; Riccardi, R. (2012)
Management of children with Thrombocytopenia-absent radius syndrome: An institutional experience.
in Journal of paediatrics and child health (Print); WILEY-BLACKWELL, MALDEN 02148,MA (Stati Uniti d'America)
(literal)
- Http://www.cnr.it/ontology/cnr/pubblicazioni.owl#autori
- Coccia, P.; Ruggiero, A.; Mastrangelo, S.; Attinà, G.; Scalzone, M.; Pittiruti, M.; Zampino, G.; Maurizi, P.; Riccardi, R. (literal)
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- Article first published online: 19 JUL 2011 - doi:10.1111/j.1440-1754.2011.02069.x (literal)
- Http://www.cnr.it/ontology/cnr/pubblicazioni.owl#numeroFascicolo
- Note
- ISI Web of Science (WOS) (literal)
- Http://www.cnr.it/ontology/cnr/pubblicazioni.owl#affiliazioni
- Coccia, P.; Ruggiero, A.; Mastrangelo, S.; Attinà, G.; Scalzone, M.; Maurizi, P.; Riccardi, R.: Univ Cattolica Sacro Cuore, Div Paediat Oncol, I-00168 Rome, Italy
Pittiruti, M.: Univ Cattolica Sacro Cuore, Dept Surg, I-00168 Rome, Italy
Zampino, G.: Univ Cattolica Sacro Cuore, Dept Paediat, I-00168 Rome, Italy (literal)
- Titolo
- Management of children with Thrombocytopenia-absent radius syndrome: An institutional experience. (literal)
- Abstract
- Aim: Thrombocytopenia-absent radius (TAR) syndrome is characterised by bilateral absence of the radii in the presence of both thumbs and hypomegakaryocytic thrombocytopenia.
Methods and results: We propose the use of long-term central venous catheters to reduce discomfort because of repeated vein punctures in search for a venous access, rendered difficult by upper limbs abnormalities.
Conclusions: It is important to improve the quality of life of affected patients. (literal)
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