Limited chronic focal encephalitis: another variant of Rasmussen syndrome? (Articolo in rivista)

Type
Label
  • Limited chronic focal encephalitis: another variant of Rasmussen syndrome? (Articolo in rivista) (literal)
Anno
  • 2008-01-01T00:00:00+01:00 (literal)
Alternative label
  • Gambardella A, Andermann F, Shorvon S, Le Piane E, Aguglia U. (2008)
    Limited chronic focal encephalitis: another variant of Rasmussen syndrome?
    in Neurology; Lippincott Williams & Wilkins, Philadelphia (Stati Uniti d'America)
    (literal)
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  • Gambardella A, Andermann F, Shorvon S, Le Piane E, Aguglia U. (literal)
Pagina inizio
  • 374 (literal)
Pagina fine
  • 377 (literal)
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  • Corresponding author: Prof. Antonio Gambardella, email: a.gambardella@isn.cnr.i (literal)
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  • 70 (literal)
Rivista
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  • 4 (literal)
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  • 5 (literal)
Note
  • ISI Web of Science (WOS) (literal)
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  • Institute of Neurology (A.G.), University Magna Graecia Catanzaro, Italy; Montreal Neurological Institute (F.A.), Montreal PQ, Canada; Institute of Neurology (S.S.), National Hospital for Neurology and Neurosurgery, Queen Square, London, UK; Regional Epilepsy Center (E.L.P., U.A.), Azienda Ospedaliera Reggio Calabria, Italy. (literal)
Titolo
  • Limited chronic focal encephalitis: another variant of Rasmussen syndrome? (literal)
Abstract
  • OBJECTIVE: To describe a more limited and less malignant form of Rasmussen encephalitis (RE). METHODS: Three subjects (all women; 37, 31, and 32 years of age) developed childhood or late onset chronic focal encephalitis, with a relatively nonprogressive form of the disorder. RESULTS: In our patients, clinical features were dominated by partial seizures without marked focal motor deficit and in two with choreo-dystonic movements. The diagnosis of RE was supported by histologic examination and anatomic and functional MRI. CONCLUSIONS: These cases extend the phenotypic presentations of Rasmussen encephalitis and confirm Theodore Rasmussen's suggestion that there may be mild and nonprogressive forms of the disease. (literal)
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