http://www.cnr.it/ontology/cnr/individuo/prodotto/ID50057
Group I metabotropic glutamate receptors: a role in neurodevelopmental disorders? (Articolo in rivista)
- Type
- Label
- Group I metabotropic glutamate receptors: a role in neurodevelopmental disorders? (Articolo in rivista) (literal)
- Anno
- 2007-01-01T00:00:00+01:00 (literal)
- Http://www.cnr.it/ontology/cnr/pubblicazioni.owl#doi
- 10.1007/s12035-007-0022-1 (literal)
- Alternative label
Catania MV, D'Antoni S, Bonaccorso CM, Aronica E, Bear MF, Nicoletti F. (2007)
Group I metabotropic glutamate receptors: a role in neurodevelopmental disorders?
in Molecular neurobiology
(literal)
- Http://www.cnr.it/ontology/cnr/pubblicazioni.owl#autori
- Catania MV, D'Antoni S, Bonaccorso CM, Aronica E, Bear MF, Nicoletti F. (literal)
- Pagina inizio
- Pagina fine
- Http://www.cnr.it/ontology/cnr/pubblicazioni.owl#numeroVolume
- Rivista
- Http://www.cnr.it/ontology/cnr/pubblicazioni.owl#pagineTotali
- Http://www.cnr.it/ontology/cnr/pubblicazioni.owl#descrizioneSinteticaDelProdotto
- Pubblicazione scientifica- invited review (literal)
- Note
- ISI Web of Science (WOS) (literal)
- Http://www.cnr.it/ontology/cnr/pubblicazioni.owl#affiliazioni
- ISN-CNR, Oasi Maria SS-Troina (EN), Massachusetts Institute of Technology, Boston USA, University of Amsterda, University of Rome-La Sapienza (literal)
- Titolo
- Group I metabotropic glutamate receptors: a role in neurodevelopmental disorders? (literal)
- Abstract
- Group I metabotropic glutamate receptors (mGlu1 and mGlu5) are coupled to
polyphosphoinositide hydrolysis and are involved in activity-dependent forms of
synaptic plasticity, both during development and in the adult life. Group I mGlu
receptors can also regulate proliferation, differentiation, and survival of
neural stem/progenitor cells, which further support their role in brain
development. An exaggerated response to activation of mGlu5 receptors may
underlie synaptic dysfunction in Fragile X syndrome, the most common inherited
form of mental retardation. In addition, group I mGlu receptors are overexpressed
in dysplastic neurons of focal cortical dysplasia and hemimegaloencephaly, which
are disorders of cortical development associated with chronic epilepsy. Drugs
that block the activity of group I mGlu receptors (in particular, mGlu5
receptors) are potentially helpful for the treatment of Fragile X syndrome and
perhaps other neurodevelopmental disorders. (literal)
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