Hypovitaminosis D: A novel finding in primary ciliary dyskinesia (Articolo in rivista)

Type
Label
  • Hypovitaminosis D: A novel finding in primary ciliary dyskinesia (Articolo in rivista) (literal)
Anno
  • 2015-01-01T00:00:00+01:00 (literal)
Http://www.cnr.it/ontology/cnr/pubblicazioni.owl#doi
  • 10.1186/s13052-015-0119-5 (literal)
Alternative label
  • Mirra V.; Caffarelli C.; Maglione M.; Valentino R.; Perruolo G.; Mazzarella C.; Di Micco L.L.; Montella S.; Santamaria F. (2015)
    Hypovitaminosis D: A novel finding in primary ciliary dyskinesia
    in The Italian Journal of Pediatrics (Testo stamp.)
    (literal)
Http://www.cnr.it/ontology/cnr/pubblicazioni.owl#autori
  • Mirra V.; Caffarelli C.; Maglione M.; Valentino R.; Perruolo G.; Mazzarella C.; Di Micco L.L.; Montella S.; Santamaria F. (literal)
Http://www.cnr.it/ontology/cnr/pubblicazioni.owl#url
  • http://www.scopus.com/inward/record.url?eid=2-s2.0-84924073282&partnerID=q2rCbXpz (literal)
Http://www.cnr.it/ontology/cnr/pubblicazioni.owl#numeroVolume
  • 41 (literal)
Rivista
Http://www.cnr.it/ontology/cnr/pubblicazioni.owl#numeroFascicolo
  • 1 (literal)
Note
  • Scopu (literal)
Http://www.cnr.it/ontology/cnr/pubblicazioni.owl#affiliazioni
  • Department of Translational Medical Sciences, Federico II University, Via Sergio Pansini, Naples, 5-80131, Italy; Department of Pediatrics, Azienda Ospedaliera-Universitaria, University of Parma, Parma, Italy; National Council of Research, Institute of Experimental Endocrinology and Oncology, Naples, Italy (literal)
Titolo
  • Hypovitaminosis D: A novel finding in primary ciliary dyskinesia (literal)
Abstract
  • Background: A relationship between low levels of serum vitamin D and respiratory infections has been established. No study has examined the frequency and clinical relevance of vitamin D deficiency in patients with primary ciliary dyskinesia (PCD). Methods: Vitamin D levels were measured in 22 PCD patients (7 females, 10.5 years, range, 2-34 years). In PCD, pulmonary function tests (PFTs), sputum microbiology, self-reported physical activity (PA) level, and quality of life (QoL) by means of the Saint George's Respiratory Questionnaire (SGRQ), were also assessed. Results: Seventy-two percent of PCD patients were vitamin-D deficient-to-insufficient and 28% were sufficient. No differences in PFTs parameters were found between vitamin D deficiency-to-insufficiency and sufficiency groups. Patients with vitamin D deficiency-to-insufficiency had significantly higher SGRQ total scores, and thus poorer QoL (p = 0.03). Seventy-nine percent of PCD subjects had limitations in performing vigorous activities, and 53% performed less than 3 hours of PA per week. Vitamin D deficiency-to-insufficiency and sufficiency groups did not show any differences in age at PCD diagnosis or at onset of respiratory symptoms, BMI, atopy, current asthma or bronchiectasis. However, 79% of patients with bronchiectasis had vitamin D deficiency-to-insufficiency. No differences were found in the rate of positive sputum cultures and in the number of antibiotic courses between the two groups. Conclusions: Hypovitaminosis D is common in PCD patients, and is associated with poorer QoL. We recommend the assessment and treatment of hypovitaminosis D to be included in the routine management of PCD. (literal)
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