Genetically determined lymphopenia and autoimmune manifestations. (Articolo in rivista)

Type
Label
  • Genetically determined lymphopenia and autoimmune manifestations. (Articolo in rivista) (literal)
Anno
  • 2008-01-01T00:00:00+01:00 (literal)
Http://www.cnr.it/ontology/cnr/pubblicazioni.owl#doi
  • 10.1016/j.coi.2008.02.001 (literal)
Alternative label
  • Villa A, Marrella V, Rucci F, Notarangelo LD. (2008)
    Genetically determined lymphopenia and autoimmune manifestations.
    in Current opinion in immunology
    (literal)
Http://www.cnr.it/ontology/cnr/pubblicazioni.owl#autori
  • Villa A, Marrella V, Rucci F, Notarangelo LD. (literal)
Pagina inizio
  • 318 (literal)
Pagina fine
  • 324 (literal)
Http://www.cnr.it/ontology/cnr/pubblicazioni.owl#numeroVolume
  • 20 (literal)
Rivista
Note
  • ISI Web of Science (WOS) (literal)
Http://www.cnr.it/ontology/cnr/pubblicazioni.owl#affiliazioni
  • Istituto di Ricerca Genetica e Biomedica, CNR (literal)
Titolo
  • Genetically determined lymphopenia and autoimmune manifestations. (literal)
Abstract
  • Hypomorphic defects of V(D)J recombination in humans lead to residual T cell development. In these lymphopenic conditions, homeostatic lymphocyte proliferation occurs, and key mechanisms that normally maintain host tolerance are altered, allowing peripheral expansion of oligoclonal and autoreactive T cells. Recently described murine models support this notion. This review describes human and murine situations, in which genetically determined T and B cell lymphopenia is associated with autoimmune manifestations. (literal)
Prodotto di
Autore CNR

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