A huge malignant perivascular epithelioid cell tumor (PEComa) of the uterine cervix and vagina (Articolo in rivista)

Type
Label
  • A huge malignant perivascular epithelioid cell tumor (PEComa) of the uterine cervix and vagina (Articolo in rivista) (literal)
Anno
  • 2014-01-01T00:00:00+01:00 (literal)
Http://www.cnr.it/ontology/cnr/pubblicazioni.owl#doi
  • 10.1016/j.prp.2013.10.003 (literal)
Alternative label
  • Natella, Valentina; Merolla, Francesco; Giampaolino, Pierluigi; Bifulco, Giuseppe; Mainenti, Pier Paolo; Insabato, Luigi (2014)
    A huge malignant perivascular epithelioid cell tumor (PEComa) of the uterine cervix and vagina
    in Pathology, research and practice (Print)
    (literal)
Http://www.cnr.it/ontology/cnr/pubblicazioni.owl#autori
  • Natella, Valentina; Merolla, Francesco; Giampaolino, Pierluigi; Bifulco, Giuseppe; Mainenti, Pier Paolo; Insabato, Luigi (literal)
Pagina inizio
  • 186 (literal)
Pagina fine
  • 188 (literal)
Http://www.cnr.it/ontology/cnr/pubblicazioni.owl#url
  • http://www.scopus.com/record/display.url?eid=2-s2.0-84893723811&origin=inward (literal)
Http://www.cnr.it/ontology/cnr/pubblicazioni.owl#numeroVolume
  • 210 (literal)
Rivista
Http://www.cnr.it/ontology/cnr/pubblicazioni.owl#numeroFascicolo
  • 3 (literal)
Note
  • Scopu (literal)
Http://www.cnr.it/ontology/cnr/pubblicazioni.owl#affiliazioni
  • Universita degli Studi di Napoli Federico II; Consiglio Nazionale delle Ricerche (literal)
Titolo
  • A huge malignant perivascular epithelioid cell tumor (PEComa) of the uterine cervix and vagina (literal)
Abstract
  • Perivascular epithelioid cell tumors (PEComas) are a family of rare mesenchymal neoplasms, including angiomyolipoma, clear-cell \"sugar\" tumor of the lung and extrapulmonary sites, lymphangioleiomyomatosis, clear-cell myomelanocytic tumor of the falciform ligament/ligamentum teres, and clear-cell tumors at various other anatomic sites.These tumors are characterized by a proliferation of epithelioid cells with clear to eosinophilic cytoplasm, perivascular distribution, and coexpression of myogenic and melanocytic markers.PEComas show a female predominance, occur with some frequency in the gynecological tract, and have an unpredictable biological behavior.We report a case of a huge malignant PEComa arising from the uterine cervix and vagina. To the best of our knowledge, only 6 cases of PEComa in the cervix and 2 cases in the vagina have been reported in the literature. © 2013 Elsevier GmbH. (literal)
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